Neurofibromatosis of head of pancreas: Obstructive jaundice

A 43-year-old patient from the provinces was suffering from Recklinghausen's disease with a 2-monthevolution cold obstructive jaundice. Paraclinic preoperative exploration showed complete biliary extrahepatic obstruction and considerable dilatation of intrahepatic biliary tract clearly shown by...

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Bibliographic Details
Authors: Fronzutti, Agustín, Lorenzelli, Amílcar, Segal, Marcos, Rieppi, Leo, Rodríguez De Vecchi, Victoriano
Format: article
Status:Published version
Publication Date:1978
Country:Uruguay
Institution:Sociedad de Cirugía del Uruguay
Repository:Revista Cirugía del Uruguay
Language:Spanish
OAI Identifier:oai:ojs2.revista.scu.org.uy:article/2974
Online Access:https://revista.scu.org.uy/index.php/cir_urug/article/view/2974
Access Level:Open access
Keyword:neoplasias pancreáticas
pancreatic neoplasms
Description
Summary:A 43-year-old patient from the provinces was suffering from Recklinghausen's disease with a 2-monthevolution cold obstructive jaundice. Paraclinic preoperative exploration showed complete biliary extrahepatic obstruction and considerable dilatation of intrahepatic biliary tract clearly shown by studies performed by conventional scintillogTaphic methods and by Bengal Rose. These methods of study are of considerable importance. Surgical e.xploration showed a tumor in the head of the pancreas which compressed the intra pancreatic biliary duct and diffuse peritoneal tumoral formations which histol'ogy defines as Neurofibromas. Cholecystojejunostomy was performed and immediate evolution was good, distant results are unknown. The papercontains a review of literature which indicates how rare this location is, since ours seems to be the first case of pancreatic location with obstructive jaundice.There follows a discussion of evolutive possibilities of this disease, with special emphasis on the risk of its becoming malign; the conclusion is that whenever possible the ideal treatment in such cases is ressection.