Solid pseudopapillary tumor of the pancreas
Introduction: Solid pseudopapillary tumors of the pancreas (SPTs) are uncommon tumors usually affecting young women in their twenties and thirties, suggesting hormonal factors to be involved in their pathogenesis. It was first described by Frantz in 1959. The vast majority of SPTs are indolent neopl...
| Autores: | , , |
|---|---|
| Tipo de recurso: | artículo |
| Estado: | Versión publicada |
| Fecha de publicación: | 2008 |
| País: | Brasil |
| Institución: | Sociedade Brasileira de Medicina de Família e Comunidade (SBMFC) |
| Repositorio: | Revista Brasileira de Medicina de Família e Comunidade (Online) |
| Idioma: | portugués |
| OAI Identifier: | oai:ojs.rbmfc.org.br:article/196 |
| Acceso en línea: | https://rbmfc.org.br/rbmfc/article/view/196 |
| Access Level: | acceso abierto |
| Palabra clave: | Pancreatic Neoplasms Neoplasias Pancreáticas |
| Sumario: | Introduction: Solid pseudopapillary tumors of the pancreas (SPTs) are uncommon tumors usually affecting young women in their twenties and thirties, suggesting hormonal factors to be involved in their pathogenesis. It was first described by Frantz in 1959. The vast majority of SPTs are indolent neoplasms. Metastases are rare and resection of the tumor when possible is curative in most cases. Case report: We report a case of a 13-year-old white girl. The clinical aspects of this case were atypical due to the appearance of symptoms associated with direct trauma and increase of the abdominal volume. Discussion: The body and tail of the pancreas are more frequently affected. The survival rate even after liver metastasis is good. Conclusion: Surgery is the mainstay of treatment. Complete resection of the tumor is usually achieved. Extensive lymphatic dissection or more radical local approaches are not indicated by most studies. |
|---|