Leber’s congenital amaurosis. Case report

Leber’s congenital amaurosis is an heterogeneous and genetic clinical disorder characterized by severe loss of vision at birth. It accounts for 10 to 18% of congenital blindness cases. Some patients exhibit solely retinal blindness and show evidence of multi-systemic involvement. The presentation of...

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Detalles Bibliográficos
Autores: Quintino Cintora, Elizabeth, López Morales, Patricia Marcela, Mendoza Rosas, Vicente
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2019
País:México
Institución:UNIVERSIDAD NACIONAL AUTÓNOMA DE MÉXICO
Repositorio:Revista Odontológica Mexicana
Idioma:español
OAI Identifier:oai:ojs.pkp.sfu.ca:article/69530
Acceso en línea:https://revistas.unam.mx/index.php/rom/article/view/69530
Access Level:acceso abierto
Palabra clave:Leber’s congenital amaurosis
congenital blindness
Descripción
Sumario:Leber’s congenital amaurosis is an heterogeneous and genetic clinical disorder characterized by severe loss of vision at birth. It accounts for 10 to 18% of congenital blindness cases. Some patients exhibit solely retinal blindness and show evidence of multi-systemic involvement. The presentation of this case includes bibliographic review of the subject, presentation of a clinical case and description of the importance of stomatologic handling of these patients. Knowledge and understanding of the disease as well as treatment sequels are paramount.