Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients

Article disponible en castellà: http://hdl.handle.net/10230/61229

Detalles Bibliográficos
Autores: Montero Menárguez, Julia, Amat Samaranch, Victoria, Puig Sanz, Lluís, Ruiz Villaverde, Ricardo, Arias Santiago, Salvador, Larrea García, Mónica, Ruiz Genao, Diana, Ferran Farrés, Marta, Schneller-Pavelescu, Luca, Romero Ferreiro, Carmen, Rivera Díaz, Raquel
Tipo de recurso: artículo
Estado:Versión publicada
Fecha de publicación:2024
País:España
Institución:Universitat Pompeu Fabra
Repositorio:Repositorio Digital de la UPF
OAI Identifier:oai:repositori.upf.edu:10230/61230
Acceso en línea:http://hdl.handle.net/10230/61230
http://dx.doi.org/10.1016/j.ad.2024.02.019
Access Level:acceso abierto
Palabra clave:Pityriasis rubra pilaris
Biologic agents
Erythroderma
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spelling Pityriasis rubra pilaris: a multicentric case series of 65 spanish patientsMontero Menárguez, JuliaAmat Samaranch, VictoriaPuig Sanz, LluísRuiz Villaverde, RicardoArias Santiago, SalvadorLarrea García, MónicaRuiz Genao, DianaFerran Farrés, MartaSchneller-Pavelescu, LucaRomero Ferreiro, CarmenRivera Díaz, RaquelPityriasis rubra pilarisBiologic agentsErythrodermaArticle disponible en castellà: http://hdl.handle.net/10230/61229Introduction: PRP is a rare entity of unknown etiopathogenesis. Lack of management guidelines makes it a challenge for clinicians. Objective: To add our experience to increase evidence about PRP. Methods: We performed a retrospective, descriptive and multicentric study of 65 patients with PRP, being the largest European case series of patients with PRP. Results: PRP was more frequent in male patients with an average age of 51 years, but erythrodermic forms presented in older patients (average age 61 years). Six (75%) paediatric patients and ten (60%) non-erythrodermic adults controlled their disease with topical corticosteroids. On the contrary, 26 (68%) erythrodermic patients required biologic therapy as last and effective therapy line requiring an average of 6.5 months to achieve complete response. Conclusion: Our study showed a statistical difference in terms of outcome and response to treatment between children or patients with limited disease and patients who develop erythroderma.Elsevier202420242024info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfapplication/pdfhttp://hdl.handle.net/10230/61230http://dx.doi.org/10.1016/j.ad.2024.02.019reponame:Repositorio Digital de la UPFinstname:Universitat Pompeu FabraInglésActas Dermosifiliogr. 2024 Sep;115(8):t761-t5© 2024 AEDV. Published by Elsevier España, S.L.U. This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).http://creativecommons.org/licenses/by-nc-nd/4.0/info:eu-repo/semantics/openAccessoai:repositori.upf.edu:10230/612302026-06-12T07:21:37Z
dc.title.none.fl_str_mv Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
title Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
spellingShingle Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
Montero Menárguez, Julia
Pityriasis rubra pilaris
Biologic agents
Erythroderma
title_short Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
title_full Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
title_fullStr Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
title_full_unstemmed Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
title_sort Pityriasis rubra pilaris: a multicentric case series of 65 spanish patients
dc.creator.none.fl_str_mv Montero Menárguez, Julia
Amat Samaranch, Victoria
Puig Sanz, Lluís
Ruiz Villaverde, Ricardo
Arias Santiago, Salvador
Larrea García, Mónica
Ruiz Genao, Diana
Ferran Farrés, Marta
Schneller-Pavelescu, Luca
Romero Ferreiro, Carmen
Rivera Díaz, Raquel
author Montero Menárguez, Julia
author_facet Montero Menárguez, Julia
Amat Samaranch, Victoria
Puig Sanz, Lluís
Ruiz Villaverde, Ricardo
Arias Santiago, Salvador
Larrea García, Mónica
Ruiz Genao, Diana
Ferran Farrés, Marta
Schneller-Pavelescu, Luca
Romero Ferreiro, Carmen
Rivera Díaz, Raquel
author_role author
author2 Amat Samaranch, Victoria
Puig Sanz, Lluís
Ruiz Villaverde, Ricardo
Arias Santiago, Salvador
Larrea García, Mónica
Ruiz Genao, Diana
Ferran Farrés, Marta
Schneller-Pavelescu, Luca
Romero Ferreiro, Carmen
Rivera Díaz, Raquel
author2_role author
author
author
author
author
author
author
author
author
author
dc.subject.none.fl_str_mv Pityriasis rubra pilaris
Biologic agents
Erythroderma
topic Pityriasis rubra pilaris
Biologic agents
Erythroderma
description Article disponible en castellà: http://hdl.handle.net/10230/61229
publishDate 2024
dc.date.none.fl_str_mv 2024
2024
2024
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
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dc.identifier.none.fl_str_mv http://hdl.handle.net/10230/61230
http://dx.doi.org/10.1016/j.ad.2024.02.019
url http://hdl.handle.net/10230/61230
http://dx.doi.org/10.1016/j.ad.2024.02.019
dc.language.none.fl_str_mv Inglés
language_invalid_str_mv Inglés
dc.relation.none.fl_str_mv Actas Dermosifiliogr. 2024 Sep;115(8):t761-t5
dc.rights.none.fl_str_mv http://creativecommons.org/licenses/by-nc-nd/4.0/
info:eu-repo/semantics/openAccess
rights_invalid_str_mv http://creativecommons.org/licenses/by-nc-nd/4.0/
eu_rights_str_mv openAccess
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application/pdf
dc.publisher.none.fl_str_mv Elsevier
publisher.none.fl_str_mv Elsevier
dc.source.none.fl_str_mv reponame:Repositorio Digital de la UPF
instname:Universitat Pompeu Fabra
instname_str Universitat Pompeu Fabra
reponame_str Repositorio Digital de la UPF
collection Repositorio Digital de la UPF
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